Summary
An unusual case of Sjögren's syndrome presenting with severe anemia as the predominant clinical feature is described. Histological examination of a bone marrow biopsy specimen demonstrated that the patient's anemia was caused by myelitis and vasculitis of the small intraosseous vessels.
Our report might stimulate a more thorough investigation of bone marrow in patients with connective tissue diseases and anemia.
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Abbreviations
- C. luciliae:
-
Crithidia luciliae
- El. v. Gi.:
-
Elastica — van Gieson
- HE:
-
hematoxylin-eosin
- HEp:
-
human epithelial carcinoma
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Poralla, T., Trautmann, F., Rumpelt, H.J. et al. A case of sjögren's syndrome with severe anemia due to myelitis. Klin Wochenschr 64, 92–95 (1986). https://doi.org/10.1007/BF01784137
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DOI: https://doi.org/10.1007/BF01784137