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Wegener's granulomatosis presenting as diffuse pulmonary hemorrhage

Abstract

A 35-year-old woman experienced diffuse intraalveolar haemorrhage with respiratory distress and acute renal failure. Renal histology and evolution confirmed Wegener's granulomatosis. Early use of immunosuppressive drugs allowed weaning from mechanical ventilation and temporary improvement of the renal failure. A review of the literature emphazises the rarity of alveolar hemorrhage as an initial symptom of Wegener's granulomatosis and the necessity of aggressive management.

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Misset, B., Glotz, D., Escudier, B. et al. Wegener's granulomatosis presenting as diffuse pulmonary hemorrhage. Intensive Care Med 17, 118–120 (1991). https://doi.org/10.1007/BF01691435

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  • DOI: https://doi.org/10.1007/BF01691435

Key words

  • Wegener's granulomatosis
  • Alveolar haemorrhage