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Familiärer Panhypopituitarismus

Familial Panhypopituitarism

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Summary

Two Italian brothers showed identical subsequent loss of anterior pituitary function during the first decades of their life, developing panhypopituitarism. The investigations carried out indicate that in this family the etiology is hereditary in nature, being X-chromosomal recessive or autosomal recessive, with the defect located at the level of either the hypothalamus or the pituitary gland

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Abbreviations

ACTH:

Adrenocorticotropes Hormon

CRH:

Corticotropin-Releasing-Hormon

FSH:

Follikelstimulierendes Hormon

GRF:

Growth-Hormon-Releasing-Hormon

LH-RH:

Gonadotropin-Releasing-Hormon

TRH:

Thyreotropin-Releasing-Hormon

TSH:

Thyreotropes Hormon

STH:

Somatotropes Hormon

SDS:

Standard-Deviation-Score

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Authors and Affiliations

  1. Abteilung Endokrinologie der Medizinischen Klinik, Universität Essen, Deutschland

    D. Hamann, Th. Olbricht, B. P. Hauffa & D. Reinwein

  2. Abteilung Endokrinologie der Medizinischen Kinderklinik, Universität Essen, Deutschland

    B. P. Hauffa

Authors
  1. D. Hamann
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  2. Th. Olbricht
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  3. B. P. Hauffa
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  4. D. Reinwein
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Hamann, D., Olbricht, T., Hauffa, B.P. et al. Familiärer Panhypopituitarismus. Klin Wochenschr 69, 725–730 (1991). https://doi.org/10.1007/BF01649443

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  • DOI: https://doi.org/10.1007/BF01649443

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