Abstract
The long-term results of surgical treatment of biliary atresia are presented from a series of 111 “noncorrectable” cases treated by the Kasai procedure. Thirty-four patients displayed some degree of restoration of bile flow for at least 1 year after surgery. Almost all of them still have some manifestations of cholestasis, abnormal intrahepatic bile ducts, persistent hepatic fibrosis, or portal hypertension. Despite this continuous liver dysfunction, many of these patients are able to carry on an almost normal life.
Résumé
Nous présentons, par une série de 111 cas d'atrésie biliaire dite “non corrigible”, les résultats à longue échéance de l'opération de Kasai. L'écoulement de bile a été rétabli pendant au moins un an, de façon plus ou moins satisfaisante, chez 34 malades. Presque tous ont encore des signes de cholostase, des canaux biliaires intrahépatiques à morphologie anormale, une fibrose hépatique persistante ou de l'hypertension portale. Malgré ces altérations hépatiques, de nombreux malades sont capables de mener une vie normale.
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Odièvre, M. Long-term results of surgical treatment of biliary atresia. World J. Surg. 2, 589–593 (1978). https://doi.org/10.1007/BF01556053
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DOI: https://doi.org/10.1007/BF01556053