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Chronic recurrent pancreatitis secondary to a submucosal ampullary tumor in a patient with neurofibromatosis

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Summary

We report a 45-year-old nonalcoholic patient with Von Recklinghausen's disease and chronic recurrent pancreatitis. On endoscopy, a benign-appearing submucosal tumor surrounded the papilla of Vater. Cannulation of the pancreatic duct showed a dilated ductal system with subsequent delayed drainage. Endoscopic manometry revealed elevated sphincter of Oddi pressures. Endoscopic sphincterotomy resulted in immediate normal drainage of the pancreatic duct and in subsequent clinical improvement.

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Authors and Affiliations

  1. Departments of Medicine and Radiology, Medical College of Wisconsin, Milwaukee, Wisconsin

    P. J. Kahrilas MD, W. J. Hogan MD, J. E. Geenen MD, E. T. Stewart MD, W. J. Dodds MD & R. C. Arndorfer

  2. St. Lukes Hospital, Racine, Wisconsin

    P. J. Kahrilas MD, W. J. Hogan MD, J. E. Geenen MD, E. T. Stewart MD, W. J. Dodds MD & R. C. Arndorfer

Authors
  1. P. J. Kahrilas MD
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  2. W. J. Hogan MD
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  3. J. E. Geenen MD
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  4. E. T. Stewart MD
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  5. W. J. Dodds MD
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  6. R. C. Arndorfer
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Kahrilas, P.J., Hogan, W.J., Geenen, J.E. et al. Chronic recurrent pancreatitis secondary to a submucosal ampullary tumor in a patient with neurofibromatosis. Digest Dis Sci 32, 102–107 (1987). https://doi.org/10.1007/BF01296695

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  • DOI: https://doi.org/10.1007/BF01296695

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