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Morgagni hernia in a patient with Morquio syndrome

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Summary

Morgagni hernia is a type of congenital diaphragmatic hernia which constitutes 2–6% of congenital diaphragmatic hernia cases. Morquio syndrome, a type of lysosomal hydrolase deficiency, results in keratan sulphate accumulation and skeletal dystrophy. Other anomalies such as cardiac anomalies and trisomy 21 may accompany the Morquio syndrome; however Morgagni hernia has not been previously reported with this syndrome. A patient with Morquio syndrome that presented with bilateral Morgagni hernias is described. During surgery primary repair is preferred, however when there are large defects synthetic mesh grafts may also be used.

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References

  • Berman L, Stringer D, Ein SH, Shandling B (1989) The late-presenting pediatrie Morgagni hernia: A benign condition. J Pediat Surg 24: 970–972

    PubMed  Google Scholar 

  • Bragg WD, Bumpers H, Flynn W, Hsu HK, Hoover EL (1996) Morgagni hernias: an uncommon cause of chest masses in adults. Am Family Phys 54; 2021–2024

    Google Scholar 

  • Doman AN, Maroteaux P, Lyne D (1990) Spondyloepiphyseal dysplasia of Maroteaux. J Bone and Joint Surg 72-A: 1364–1369

    Google Scholar 

  • Potter R, Schimpl G, Sorantin E, Fritz K, Landler U (1992) Delayed presentation of congenital diaphragmatic hernia. Pediat Radiol 22: 187–191

    PubMed  Google Scholar 

  • Groff DB (1990) Diagnosis of a Morgagni hernia complicated by a previous normal chest X-ray. J Pediat Surg 25: 556–557

    PubMed  Google Scholar 

  • Hussong RL Jr, Landreneau RJ, Cole FH Jr (1997) Diagnosis and repair of a Morgagni hernia with video-assisted thoracic surgery. Ann Thorac Surg 63: 1474–5

    PubMed  Google Scholar 

  • Kheradpir MH, Ahmadi J (1988). Morgagni hernias during infancy. Int Surg 73: 257–259

    PubMed  Google Scholar 

  • Kimmelstiel FM, Holgersen LO, Hilfer C (1987) Retrosternal (Morgagni) hernia with small bowel obstruction secondary to a Richter's incarceration. J Pediat Surg 22: 998–1000

    PubMed  Google Scholar 

  • Newman L 3rd, Eubanks S, Bridges WM 2nd, Lucas G (1995) Laparoscopic diagnosis and treatment of Morgagni hernia. Surg Laparosc Endosc 5: 27–31

    PubMed  Google Scholar 

  • Pokorny WJ, McGill CW, Harberg FJ (1984) Morgagni hernias during infancy: Presentation and associated anomalies. J Pediat Surg 19: 394–397

    PubMed  Google Scholar 

  • Steiner Z, Mares AJ (1993) Anterolateral diaphragmatic hernia: is it a Morgagni hernia? Eur J Pediat Surg 3: 112–114

    Google Scholar 

  • Torfs CP, Curry C, Bateson TF, Honore LH (1992) A population-based study of congenital diaphragmatic hernia. Teratology 46: 555–565

    PubMed  Google Scholar 

  • Wiedemann HR (1992) Luis Morquio. Eur J Pediat 151: 549

    Google Scholar 

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Nursal, T.Z., Atli, M. & Kaynaroglu, V. Morgagni hernia in a patient with Morquio syndrome. Hernia 4, 37–39 (2000). https://doi.org/10.1007/BF01230591

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  • DOI: https://doi.org/10.1007/BF01230591

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