Summary
We report a case of association of a brain tumor with multiple colorectal polyposis and offer an analysis of the relevant literature with a view to revising the classification of the syndrome in relation to familial multiple polyposis and Gardner's syndrome. Differences emerged, depending on the brain tumor type, which suggests that this association may be classified as two distinct syndromes.
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Cervoni, L., Celli, P., Tarantino, R. et al. Turcot's syndrome: Case report and review of the classification. J Neuro-Oncol 23, 63–66 (1995). https://doi.org/10.1007/BF01058460
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DOI: https://doi.org/10.1007/BF01058460