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Pediatric Radiology

, Volume 8, Issue 4, pp 251–253 | Cite as

A case of neurofibromatosis with severe osseous disease of the thoracic spine

  • Vibeke Hvorslev
  • Susanne Reiter
Short Reports

Abstract

A case of neurofibromatosis in a 7-year-old boy from Greenland is presented. The patient suddenly developed a severe thoracic scoliosis because of a total luxation of the upper thoracic vertebrae caused by erosion from soft tissue tumours in the region. Tomography revealed the bone changes, and CT whole-body scanning showed the extent of the soft tissue tumours and also the destruction of the vertebrae. The diagnosis was verified by biopsy.

Key words

Neurofibromatosis Mb. Recklinghausen Congenital neurocutaneous syndrome 

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Copyright information

© Springer-Verlag 1979

Authors and Affiliations

  • Vibeke Hvorslev
    • 1
    • 2
  • Susanne Reiter
    • 1
    • 2
  1. 1.Department of Pediatrics, RigshospitaletUniversity of CopenhagenCopenhagenDenmark
  2. 2.Department of Diagnostic Radiology, RigshospitaletUniversity of CopenhagenCopenhagenDenmark

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