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Pediatric Radiology

, Volume 3, Issue 1, pp 1–5 | Cite as

Pyloro-duodenal atresia

A report of three families with several similarly affected children
  • R. E. Melhem
  • G. Salem
  • H. Mishalany
  • M. Slim
  • V. M. Der Kaloustian
Originals

Abstract

Seven patients born with pyloro-duodenal atresia are reported, one had an additional atresia of the small and large bowel, and another had a pneumoperitoneum probably secondary to rupture of the stomach. All patients had the same radiological findings and had no air distal to the pylorus. Consanguinity was elicited in four and a familial incidence of an identical malformation in siblings in six. 6 of the 7 patients were operated on and 4 are living and well 6 months to 5 years later. This report raises the total number of published cases of pyloro-duodenal atresia to 46, and provides further evidence for an autosomal recessive mode of inheritance.

Key words

Pylorus atresia newborn vomiting 

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Copyright information

© Springer-Verlag 1975

Authors and Affiliations

  • R. E. Melhem
    • 1
    • 2
  • G. Salem
    • 1
    • 2
  • H. Mishalany
    • 1
    • 2
  • M. Slim
    • 1
    • 2
  • V. M. Der Kaloustian
    • 1
    • 2
  1. 1.Department of RadiologyAmerican University Medical CenterBeirutLebanon
  2. 2.Department of Pediatrics and SurgeryAmerican University Medical CenterBeirutLebanon

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