Pediatric Radiology

, Volume 11, Issue 2, pp 87–90 | Cite as

Familial osteopathia striata with cranial condensation

  • H. Cortina
  • A. Vallcanera
  • J. Vidal


For the first time in the literature, we describe a dominant autosomal inheritance of osteopathia striata with cranial condensation. Including the patients referred to here, the total published cases is ten, sufficient to make it an independent entity. Furthermore, deafness has been detected in 50% of the cases, which gives it greater importance than a mere radiological curiosity.

Key Words

Osteopathia striata Osteopetrosis Pycnodysostosis Metaphyseal dysplasia Deatness Osteopoikilia Melorheostosis 


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Copyright information

© Springer-Verlag 1981

Authors and Affiliations

  • H. Cortina
    • 1
  • A. Vallcanera
    • 1
  • J. Vidal
    • 1
  1. 1.Clinica Infantil, Servicio de RadiodiagnósticoCiudad Sanitaria de la SS “La Fe”ValenciaSpain

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