X-linked congenital retinoschisis

  • Ulrich Kellner
  • Stefanie Brümmer
  • Michael H. Foerster
  • Achim Wessing
Clinical Investigations

Abstract

The natural history and electrophysiological findings of 52 patients with X-linked congenital retinoschisis with a follow-up of up to 26 years are described. The mean visual acuity was reduced to 0.24±0.2 and remained unchanged in most patients during this time. If visual loss occurred, it usually happened in the first decennium. The complications were retinal detachments in 11% and vitreous hemorrhages in 4% of the eyes. In general, the vitreous hemorrhages resolved spontaneously. Retinal detachments were treated successfully with conventional buckling procedures. Redetachments occurred in about 40%. Prophylactic laser coagulation was of no use because it was complicated by detachment in 43% of our series. The electro-oculogram was usually normal. In addition to the known electroretinographic findings of normal a-wave and reduced b-wave amplitudes, we found prolonged b-wave latencies and implicit times, as well as a reduced 30 Hz flicker response.

Keywords

Public Health Visual Acuity Natural History Visual Loss Retinal Detachment 

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Copyright information

© Springer-Verlag 1990

Authors and Affiliations

  • Ulrich Kellner
    • 1
  • Stefanie Brümmer
    • 1
  • Michael H. Foerster
    • 1
  • Achim Wessing
    • 1
  1. 1.Zentrum für Augenheilkunde der Universität EssenEssen 1Germany

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