Abstract
A male infant with scaphoid megalourethra, which is a rare congenital anomaly, is presented. At birth he exhibited a grossly swollen, malformed penis and cryptorchidism. The corpus spongiosum was not palpable. The infant had congenital renal failure. Retrograde urethrography revealed a crescent-shaped dilatation of the anterior urethra, and the diagnosis of scaphoid megalourethra was made. Subsequent uroradiological examinations showed that there were also severe urogenital anomalies, i.e. renal hypoplasia-dysplasia, hydronephrosis, hydroureter and vesicoureteral reflux. This disorder is frequently associated with other urogenital anomalies. Therefore, once the diagnosis is reached, a careful investigation for other associated abnormalities should be undertaken.
References
Nesbitt TE (1955) Congenital megalo-urethra. J Urol 73: 839–842
Stephens FD (1963) Congenital malformations of the rectum, anus and genitourinary tracts. In: Webster R (ed) Urethral obstruction in childhood: the use of urethrography in childhood. Churchill Livingstone, Edinburgh, pp 226–240
Johnston JH, Coimbra JAM (1970) Megalourethra, J Pediatr Surg 5: 304–308
Kirchner SG, Burko H (1975) Congenital megalourethra. Pediatr Radiol 3: 89–92
Halal F, Attendu CA, Théoret G (1980) Méga-urètre, hypospadias et anus imperforé chez un nouveau-né: rôle possible du clomiphène pris par la mère. Can Med Assoc J 122: 1159–1160
Shrom SH, Cromie WJ, Duckett JW Jr (1981) Megalourethra. Urology 17: 152–156
Mortensen PHG, Johnson HW, Coleman GU, Lirenman DS, Taylor G, McLoughlin MG (1985) Megalourethra. J Urol 134: 358–361
Appel RA, Kaplan GW, Brock WA, Streit D (1986) Megalourethra. J Urol 135: 747–751
Kester RR, Mooppan UMM, Ohm HK, Kim H (1990) Congenital megalourethra. J Urol 143: 1213–1215
Reissigl A, Eberle J, Bartsch G (1991) Megalourethra. Br J Urol 68: 435–438
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Hata, A., Tsukahara, H., Shigematsu, Y. et al. Scaphoid megalourethra with multiple urogenital anomalies. Pediatr Nephrol 8, 218–220 (1994). https://doi.org/10.1007/BF00865485
Received:
Revised:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF00865485