Abstract
A child of 10 years 5 months presenting with chronic renal failure had bilateral cystic kidneys. Biopsy of a right lower-pole solid mass revealed nephroblastoma. At bilateral nephrectomy, both kidneys were both replaced by variable-sized cysts with a unifocal nephroblastoma on the right. Renal failure with nephroblastoma is uncommon and is usually either a manifestation of the Drash syndrome or a complication of chemotherapy. The need to assess both kidneys in a child with any other renal abnormality in addition to a renal mass should always be considered.
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Craver, R.D., Correa, H., Hollowell, J.G. et al. Nephroblastoma and end-stage renal failure with bilateral cystic kidneys. Pediatr Nephrol 9, 182–185 (1995). https://doi.org/10.1007/BF00860739
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DOI: https://doi.org/10.1007/BF00860739