Pediatric Nephrology

, Volume 4, Issue 3, pp 228–232 | Cite as

Cystic lymphangiectasia of the kidneys in an infant with nephrotic syndrome

  • Tej K. Mattoo
  • A. Baez Giangreco
  • Mohammad Afzal
  • Mohammad Akhtar
Original Article


Cystic lymphangiectasia of kidneys is a very rare abnormality. We report a 2-year-old boy with this disorder who also had congenital nephrotic syndrome. Unilateral nephrectomy abated the problems related to heavy proteinuria.

Key words

Cystic lymphangiectasia Congenital nephrotic syndrome 


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Copyright information

© IPNA 1990

Authors and Affiliations

  • Tej K. Mattoo
    • 1
  • A. Baez Giangreco
    • 2
  • Mohammad Afzal
    • 2
  • Mohammad Akhtar
    • 3
  1. 1.Department of Paediatric NephrologyMaternity and Children's HospitalRiyadhSaudi Arabia
  2. 2.Central Laboratory and Blood BankRiyadhSaudi Arabia
  3. 3.Electron Microscopy LaboratoryKing Faisal Specialist Hospital and Research CentreRiyadhSaudi Arabia

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