Pediatric Nephrology

, Volume 7, Issue 4, pp 375–378 | Cite as

Glomerulocystic disease: unilateral involvement of a horseshoe kidney and in trisomy 18

  • Randall D. Craver
  • Joseph Ortenberg
  • Radhakrishna Baliga
Original Article

Abstract

Two occurrences of glomerulocystic kidney disease (GCD) in children younger than 1 year are described. One child was 3 months old with trisomy 18; the other child was 6 months old with GCD localized to one side of a horseshoe kidney. Lectin and immunohistochemical studies in tissue from the second child suggested that the entire nephron may be affected in GCD. There may also be overlap of morphological features between GCD and early stages of autosomal dominant polycystic kidneys.

Key words

Glomerulocystic disease Autosomal dominant polycystic kidney disease Horseshoe kidney Trisomy 18 Renal dysplasia 

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Copyright information

© IPNA 1993

Authors and Affiliations

  • Randall D. Craver
    • 1
  • Joseph Ortenberg
    • 1
  • Radhakrishna Baliga
    • 1
  1. 1.New Orleans Children's HospitalLouisiana State University Medical CenterNew OrleansUSA

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