Summary
In a 10-year-old boy with pseudohypoparathyroidism type Ia (PHP-Ia) echocardiography detected calcifications within the ventricular septum. This is thought to be the first report of intracardiac calcifications in PHP. Echocardiography should be done routinely in all patients with this rare disorder.
Similar content being viewed by others
References
Abara S, Carranza C, Henriques L (1986) Pseudohypo-parathyroidism and hypocalcemic cardiomyopathy.Rev Chil Pediatr 57:575–579
Albright FC, Burnett CH, Smith PH, Parson W (1942) Pseudohypoparathyroidism, an example of “Seabright-Bantam syndrome.” Report of three cases.Endocrinology 30:922–932
Connor TB, Rosen RL, Blaustein MP, Applefield MM, Doyle LA (1982) Hypocalcemia precipitating congestive heart failure.N Engl J Med 307:869–872
Drezner MK, Neelon FA (1983) Pseudohypoparathyroidism. In: Stanbury JB, Wyngaarden JB, Fredrickson DS, Goldstein JL, Brown MS (eds)The Metabolic Basis of Inherited Diseases, 5th edn, McGraw-Hill, New York, pp 1508–1527
Illum F, Dupont E (1985) Prevalences of CT-detected calcifications in the basal ganglia in idiopathic hypoparathyroidism and pseudohypoparathyroidism.Neuroradiology 27:32–37
Katz JH, Dias SM, Ferguson RP (1988) Fatal cardiac calcifications secondary to primary hyperparathyroidism.Am J Med 85:122–123
Kida T, Hujita Y, Sasaki M, Inoue J (1986) Myocardial and vascular uptake of a bone tracer associated with secondary hyperparathyroidism.Eur J Nucl Med 12:151–154
Mako J, Lengyel M, Szuos J (1987) Intracardiac calcification in patients under chronic haemodialysis.Int Urol Nephrol 19:441–446
Rao DS, Antonelli R (1989) Hypercalcemia, primary hyperparathyroidism, and cardiac calcifications [Letter].Am J Med 86:364
Rostand SG, Sanders C, Kirk KA, Rutsky EA, Fraser RG (1988) Myocardial calcification and cardiac dysfunction in chronic renal failure.Am J Med 85:651–657
Spiegel AM (1989) Pseudohypoparathyroidism. In: Scriver CR, et al. (eds)The Metabolic Basis of Inherited Diseases, 6th edn. McGraw-Hill, New York, pp 2013–2027
Venkataraman PS, Han BK, Tsang RC, Daugherty CC (1983) Secondary hyperparathyroidism and bone disease in infants receiving long-term furosemide therapy.Am J Dis Child 137:1157–1161
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Schuster, V., Sandhage, K. Intracardiac calcifications in a case of pseudohypoparathyroidism type Ia (PHP-Ia). Pediatr Cardiol 13, 237–239 (1992). https://doi.org/10.1007/BF00838784
Issue Date:
DOI: https://doi.org/10.1007/BF00838784