Headache caused by craniospinal pressure dissociation in the Arnold-Chiari-syringomyelia syndrome


Two patients with Arnold-Chiari malformation, associated with syringomyelia, are described. They presented with headache caused by coughing, sneezing and straining. The pathogenesis and diagnosis are discussed. The treatment of this condition consists in a fossa posterior decompression, in some cases followed by a syringoperitoneal or a syringosubarachnoid shunt.

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Van den Bergh, R. Headache caused by craniospinal pressure dissociation in the Arnold-Chiari-syringomyelia syndrome. J Neurol 239, 263–266 (1992). https://doi.org/10.1007/BF00810349

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Key words

  • Headache
  • Arnold-Chiari malformation
  • Syringomyelia