Pediatric Cardiology

, Volume 16, Issue 3, pp 120–126 | Cite as

Cardiopulmonary performance during exercise in patients with repaired tetralogy of Fallot with absent pulmonary valve

  • N. Mulla
  • S. M. Paridon
  • W. W. Pinsky
Original Articles

Abstract

In patients with tetralogy of Fallot and absent pulmonary valve, the dilated pulmonary arteries sometimes result in bronchial compression and pulmonary symptoms due to airway obstruction, recurrent pulmonary infection, and development of bronchiectasis. After complete intracardiac repair, residual pulmonary disease may be expected to result in impaired cardiopulmonary performance during exercise. To assess this hypothesis, nine patients with tetralogy of Fallot and absent pulmonary valve underwent exercise testing and were compared to 38 patients with tetralogy of Fallot repaired using a transannular patch. All patients were exercied to maximum volition using a 1 minute incremental treadmill protocol with monitoring of pulmonary functions and expired gases. Maximal heart rate, maximal oxygen consumption, oxygen consumption at anaerobic threshold, and maximal respiratory exchange ratio were similar for the two groups. There was no significant difference for ventilation and gas exchange parameters at rest or at maximal exercise, and values for both groups were below the predicted normal for healthy subjects. Breathing reserve, however, did tend to be some-what lower in the group with tetralogy of Fallot with absent pulmonary valve. In summary, despite significant preoperative symptoms, cardiopulmonary performance during exercise in patients with tetralogy of Fallot and absent pulmonary valve is similar to patients with tetralogy of Fallot repaired with a transannular patch.

Key words

Tetralogy of Fallot Absent pulmonary valve Exercise Pulmonary function 

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Copyright information

© Springer-Verlag New York Inc 1995

Authors and Affiliations

  • N. Mulla
    • 1
  • S. M. Paridon
    • 1
  • W. W. Pinsky
    • 1
  1. 1.Division of Cardiology, Children's Hospital of MichiganWayne State University School of MedicineDetroitUSA

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