Pediatric Cardiology

, Volume 13, Issue 2, pp 104–106 | Cite as

Persistence of hypoplastic and recoarcted fifth aortic arch associated with type A aortic arch interruption: Surgical and balloon angioplasty results in an infant

  • Alexandre Graziadei Da Costa
  • Eliza Rumiko Iwahashi
  • Edmar Atik
  • Miguel Antonio Neves Rati
  • Munir Ebaid
Case Reports


A rare aortic malformation, the persistence of the fifth aortic arch (PFAA) associated with coarctation of the aorta, is reported in a 3-month-old male infant who underwent an emergency surgical intervention at 10 days of life, to relieve a severe aortic coarctation by pericardial patch technique.

A successful balloon angioplasty was performed 2 months later eliminating a recoarctation. The gradient fell from 77 mmHg to 0, but a definitive surgical intervention for recoarctation was necessary 14 months after angioplasty.

Key Words

Persistent fifth aortic arch Type A aortic interruption Balloon angioplasty Aortic coarctation 


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Copyright information

© Springer-Verlag New York Inc. 1992

Authors and Affiliations

  • Alexandre Graziadei Da Costa
    • 1
  • Eliza Rumiko Iwahashi
    • 1
  • Edmar Atik
    • 1
  • Miguel Antonio Neves Rati
    • 1
  • Munir Ebaid
    • 1
  1. 1.Paediatric Cardiology Department of Heart InstituteUniversity of São PauloSão PauloBrazil

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