Pediatric Cardiology

, Volume 14, Issue 2, pp 124–126 | Cite as

Pseudohypertension in a child with Williams syndrome

  • C. Narasimhan
  • Thomas Alexander
  • Shanker Krishnaswami
Case Reports


Pseudohypertension has often been reported in elderly subjects, but is an unusual phenomenon in children. We report the case of a 5-year-old child who presented with features of Williams syndrome (characterized by elfin facies, supravalvar aortic stenosis, and peripheral pulmonary artery stenosis). Repeated blood pressure recordings made with appropriately sized blood pressure cuffs were very high, while simultaneous intraarterial blood pressure was normal, confirming the presence of pseudohypertension. This was shown to be caused by excessively thickened arterial vessels.

Key Words

Pseudohypertension Williams syndrome 


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Copyright information

© Springer-Verlag New York Inc. 1993

Authors and Affiliations

  • C. Narasimhan
    • 1
  • Thomas Alexander
    • 1
  • Shanker Krishnaswami
    • 1
  1. 1.Department of CardiologyChristian Medical College HospitalVellore

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