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Right ventricular outflow obstruction by anomalies of the tricuspid valve: Report of a windsock diverticulum

Summary

A 9-month-old infant with a clinical diagnosis of double outlet from the right ventricle, subaortic ventricular septal defect, and muscular subpulmonary obstruction underwent surgical repair. The defect was corrected and the right ventricular infundibulum enlarged with a patch. Eight hours after the operation there was a sudden collapse which rapidly progressed to cardiac arrest and death. Postmortem examination of the heart confirmed the clinical diagnosis but noted that the subpulmonary obstruction was caused by a “windsock” deformity of the tricuspid valve which was not identified at operation. The variants of malformations of the tricuspid valve causing subpulmonary obstruction are reviewed.

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Gerlis, L.M., Ho, S.Y. & Rigby, M.L. Right ventricular outflow obstruction by anomalies of the tricuspid valve: Report of a windsock diverticulum. Pediatr Cardiol 13, 59–62 (1992). https://doi.org/10.1007/BF00788234

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  • DOI: https://doi.org/10.1007/BF00788234

Key Words

  • Congenital heart disease
  • Tricuspid valve windsock malformation
  • Subpulmonary obstruction
  • Double-outlet right ventricle
  • Ventricular septal defect