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European Journal of Pediatrics

, Volume 146, Issue 3, pp 305–308 | Cite as

Acute intermittent porphyria —an unusual cause of “surgical” abdomen

Response to proparanolol therapy
  • I. Srugo
  • E. Said
  • S. Korman
  • M. Jaffe
Case Reports

Abstract

We report a case of Acute Intermittent Porphyria which presented with acute abdominal distress, autonomic dysfunction and laboratory abnormalities. The treatment is discussed with special emphasis on the effect of large doses of Propranolol.

Key words

Acute intermittent porphyria Treatment Propranolol 

Abbreviations

AIP

acute intermittent porphyria

ALA

δ-aminolevulinic acid

COPRO

coproporphyrin

PBG

porphobilinogen

TMP-SMZ

trimethoprim-sulfasoxisole

URO

uroporphyrin

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Copyright information

© Springer-Verlag 1987

Authors and Affiliations

  • I. Srugo
    • 1
    • 2
  • E. Said
    • 1
    • 2
  • S. Korman
    • 1
    • 2
  • M. Jaffe
    • 1
    • 2
  1. 1.Department of PediatricsHaifa Medical Center (Rothschild)HaifaIsrael
  2. 2.Faculty of MedicineTechnion — Israel Institute of TechnologyHaifaIsrael

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