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Biggemann, B., Zass, R. & Wendel, U. Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin. J Inherit Metab Dis 16, 912–913 (1993). https://doi.org/10.1007/BF00714298
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DOI: https://doi.org/10.1007/BF00714298