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Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin

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Journal of Inherited Metabolic Disease

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References

  • Berry GT, Heidenreich R, Kaplan P et al (1991) Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.N Engl J Med 324: 175–179.

    Google Scholar 

  • Castellino P, Luzi L, Simonson DC, Haymond M, De Fronzo RA (1987) Effect of insulin and plasma amino acid concentrations on leucine metabolism in man.J Clin Invest 80: 1784–1793.

    Google Scholar 

  • Fiedler AE, Miller MJ, Bickel H, Cederbaum SD (1982) Phenylalanine levels in PKU following minor surgery.Am J Med Genet 11: 411–414.

    Google Scholar 

  • Tessari P, Trevisan R, Inchiostro S et al (1986) Dose-response curves of effects of insulin on leucine kinetics in humans.Am J Physiol 251: E334–342.

    Google Scholar 

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Biggemann, B., Zass, R. & Wendel, U. Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin. J Inherit Metab Dis 16, 912–913 (1993). https://doi.org/10.1007/BF00714298

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