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Journal of Inherited Metabolic Disease

, Volume 17, Issue 6, pp 753–754 | Cite as

Parenteral administration of amino acids in disorders of branched-chain amino acid metabolism

  • W. Sperl
  • D. Skladal
  • W. Endres
  • G. Speer
  • K. Groke
Short Report
  • 29 Downloads

Keywords

Public Health Internal Medicine Acid Metabolism Amino Acid Metabolism Parenteral Administration 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

References

  1. Berry GT, Heidenreich R, Kaplan P et al (1991) Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.N Engl J Med 324: 175–179.Google Scholar
  2. Kahler SG, Millington DS, Cederbaum SD et al (1989) Parenteral nutrition in propionic and methylmalonic acidemia.J Pediatr 115: 235–241.Google Scholar
  3. Thompson GN, Francis DEM, Halliday D (1991) Acute illness in maple syrup urine disease: dynamics of protein metabolism and implications for management.J Pediatr 119: 35–41.Google Scholar
  4. Townsend I, Kerr DS (1982) Total parenteral nutrition therapy of toxic maple syrup urine disease.Am J Clin Nutr 36: 359–365.Google Scholar

Copyright information

© Society for the Study of Inborn Errors of Metabolism and Kluwer Academic Publishers 1994

Authors and Affiliations

  • W. Sperl
    • 1
  • D. Skladal
    • 1
  • W. Endres
    • 1
  • G. Speer
    • 2
  • K. Groke
    • 3
  1. 1.Department of PaediatricsUniversity of InnsbruckInnsbruckAustria
  2. 2.Pharmacy of the University HospitalInnsbruckAustria
  3. 3.Leopold-Pharma Co.GrazAustria

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