Journal of Inherited Metabolic Disease

, Volume 17, Issue 6, pp 753–754 | Cite as

Parenteral administration of amino acids in disorders of branched-chain amino acid metabolism

  • W. Sperl
  • D. Skladal
  • W. Endres
  • G. Speer
  • K. Groke
Short Report
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Keywords

Public Health Internal Medicine Acid Metabolism Amino Acid Metabolism Parenteral Administration 

References

  1. Berry GT, Heidenreich R, Kaplan P et al (1991) Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.N Engl J Med 324: 175–179.Google Scholar
  2. Kahler SG, Millington DS, Cederbaum SD et al (1989) Parenteral nutrition in propionic and methylmalonic acidemia.J Pediatr 115: 235–241.Google Scholar
  3. Thompson GN, Francis DEM, Halliday D (1991) Acute illness in maple syrup urine disease: dynamics of protein metabolism and implications for management.J Pediatr 119: 35–41.Google Scholar
  4. Townsend I, Kerr DS (1982) Total parenteral nutrition therapy of toxic maple syrup urine disease.Am J Clin Nutr 36: 359–365.Google Scholar

Copyright information

© Society for the Study of Inborn Errors of Metabolism and Kluwer Academic Publishers 1994

Authors and Affiliations

  • W. Sperl
    • 1
  • D. Skladal
    • 1
  • W. Endres
    • 1
  • G. Speer
    • 2
  • K. Groke
    • 3
  1. 1.Department of PaediatricsUniversity of InnsbruckInnsbruckAustria
  2. 2.Pharmacy of the University HospitalInnsbruckAustria
  3. 3.Leopold-Pharma Co.GrazAustria

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