Journal of Inherited Metabolic Disease

, Volume 16, Issue 2, pp 280–283 | Cite as

Ceroid, lipofuscin and the ceroid-lipofuscinoses (Batten Disease)

  • R. D. Jolly
  • R. R. Dalefield
  • D. N. Palmer
NCL Symposium — Pathogenetic Mechanisms

Conclusion

The similar histochemical, fluorescent and ultrastructural appearance of some lipofuscins and the pigment of Batten disease imply some underlying common chemical feature. The similar chloroform—methanol solubility of the protein subunit c in Batten disease and the specific proteins accumulated in thyroid lipofuscin imply that disordered or delayed catabolism of hydrophobic protein may be that common feature.

Keywords

Public Health Methanol Internal Medicine Chloroform Chemical Feature 

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References

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Copyright information

© Society for the Study of Inborn Errors of Metabolism and Kluwer Academic Publishers 1993

Authors and Affiliations

  • R. D. Jolly
    • 1
  • R. R. Dalefield
    • 1
  • D. N. Palmer
    • 1
  1. 1.Department of Veterinary Pathology and Public HealthMassey UniversityPalmerston NorthNew Zealand

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