Child's Nervous System

, Volume 3, Issue 1, pp 47–49 | Cite as

Paroxysmal kinesigenic choreoathetosis

  • Shaul Harel
  • U. Yurgenson
  • M. Kutai
Case Reports


A healthy intelligent 13.5-year-old boy is reported who presented with paroxysmal kinesigenic choreoathetosis. He had had unilateral tonic spasms for 2 months. In a stressful situation, especially after a period of immobility, a sudden voluntary movement provoked a dystonic-choreoathetoic posturing of the left arm and leg. Attacks were brought on, for instance, by standing up quickly from a sitting position. They lasted only 5–10 s, without loss of consciousness and occurred up to ten times daily. Between the attacks there were no abnormalities. Family history was non-contributory. Neurological examination and laboratory findings, including repeated EEGs, were all negative. The child responded very well to phenytoin treatment and has now been completely free of dystonic attacks for a period of 9 months. The importance of early recognition of this syndrome and the differential diagnosis with reflex epilepsy and other forms of dystonic choreoathetosis is discussed.

Key words

Paroxysmal disorder Choreoathetosis Dystonia Movement disorder 


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Copyright information

© Springer-Verlag 1987

Authors and Affiliations

  • Shaul Harel
    • 1
  • U. Yurgenson
    • 1
  • M. Kutai
    • 1
  1. 1.Pediatric Neurology Unit, Division of Pediatrics, Tel Aviv Medical Center, Sackler Medical SchoolUniversity of Tel AvivTel AvivIsrael

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