Virchows Archiv A

, Volume 402, Issue 1, pp 99–106 | Cite as

Renal dysplasia of the sacral region: Metanephric dysplastic hamartoma of the sacral region

  • Cleto Cozzutto
  • Vincenzo Stracca-Pansa
  • Francesco Salano
Case Report

Summary

We believe this to be the third reported case of an unusual congenital sacral tumor-like lesion characterized histologically by the presence of dysplastic and immature renal-like tissue with a predominant glomerular and tubular structure.

This lesion appears important in the differential diagnosis of extrarenal nephroblastoma, and should be regarded as a dysplastic overgrowth.

An origin from mesonephric or metanephric remnants is suggested.

Key words

Sacral region Retroperitoneum Kidney congenital abnormalities Kidney, dysplasia Kidney, neoplasms 

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Copyright information

© Springer-Verlag 1983

Authors and Affiliations

  • Cleto Cozzutto
    • 1
  • Vincenzo Stracca-Pansa
    • 2
  • Francesco Salano
    • 3
  1. 1.Departments of PathologyGiannina Gaslini Institute Children's and Women's HospitalGenoaItaly
  2. 2.Ospedale CivileVicenza
  3. 3.Department of SurgeryOspedale CivileVicenzaItaly

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