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Virchows Archiv A

, Volume 404, Issue 3, pp 275–287 | Cite as

Malignant epithelioid hemangioendothelioma of the liver, spreading through the hepatic veins

  • Masashi Fukayama
  • Zenrou Nihei
  • Touichirou Takizawa
  • Kenji Kawaguchi
  • Hideharu Harada
  • Morio Koike
Article

Summary

A case of malignant epithelioid hemangioendothelioma of the liver mimicking veno-occlusive disease is reported. The histological, ultrastructural, and immunohistochemical features of the present case indicate striking similarities to epithelioid hemangioendothelioma (EHE) of the soft parts described by Weiss and Enzinger. Tumour metastasis to the lung gave a picture closely resembling intravascular bronchiolo-alveolar tumour (IVBAT) of the lung. EHE of the liver is considered to be a unique type of hepatic endothelial neoplasm behaving as a low grade malignant tumour with a veno-occlusive process which has rarely been described, and had previously been classified as other diseases or neoplasms.

Key words

Epithelioid hemangioendothelioma Liver IVBAT Veno-occlusive disease 

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Copyright information

© Springer-Verlag 1984

Authors and Affiliations

  • Masashi Fukayama
    • 1
  • Zenrou Nihei
    • 1
  • Touichirou Takizawa
    • 1
  • Kenji Kawaguchi
    • 1
  • Hideharu Harada
    • 2
  • Morio Koike
    • 1
  1. 1.Department of PathologyTokyo Metropolitan Komagome HospitalBunkyo-ku, Tokyo
  2. 2.Department of MedicineTokyo Metropolitan Komagome HospitalTokyoJapan

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