Acta Neuropathologica

, Volume 48, Issue 1, pp 11–17 | Cite as

Möbius syndrome

Neuropathologic observations
  • J. Towfighi
  • K. Marks
  • E. Palmer
  • R. Vannucci
Original Works

Summary

Neuropathologic findings in an infant with congenital right facial and bilateral lateral recturs palsy (Möbius syndrome) are presented. Multiple microscopic foci of necrosis were found in the lower pontine tegmentum, involving the region of the intramedullary course of 6th and 7th cranial nerves. The significance of pathologic findings in this infant and 14 additional published cases of Möbius syndrome is discussed.

Key words

Möbius Congenital Cranial nerve Palsy Pons 

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Copyright information

© Springer-Verlag 1979

Authors and Affiliations

  • J. Towfighi
    • 1
  • K. Marks
    • 2
  • E. Palmer
    • 3
  • R. Vannucci
    • 2
  1. 1.College of Medicine, Department of PathologyThe Pennsylvania State UniversityHersheyUSA
  2. 2.College of Medicine, Department of Pediatrics (Divisions of Neurology and Newborn Medicine)The Pennsylvania State UniversityHersheyUSA
  3. 3.College of Medicine, Department of Surgery (Ophthalmology)The Pennsylvania State UniversityHersheyUSA

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