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Acta Neuropathologica

, Volume 4, Issue 6, pp 640–645 | Cite as

Late infantile familial metachromatic leucodystrophy in minks

  • Erna Christensen
  • Birthe Palludan
Original Investigations

Summary

Late infantile familial metachromatic leucodystrophy is described among mink kits from a farm breeding standard minks. The findings suggest that the disease is hereditary because of the presence of a recessive sublethal factor. Both the biological age, the clinical picture and the histological findings are in accordance with the findings in human cases. It counts also for the result of the sparse histochemical examinations carried out until now.

Keywords

Public Health Clinical Picture Histological Finding Human Case Histochemical Examination 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Zusammenfassung

Die nach-infantile Form von familiärer metachromatischer Leukodystrophie wird an jungen Nerzen aus einer Nerzzuchtfarm beschrieben. Die Befunde weisen auf die Erblichkeit der Krankheit zufolge eines recessiven Subletalfaktors hin. Biologisches Alter, klinisches Bild und histologische Befunde stehen mit den Befunden von menschlichen Krankheitsfällen im Einklang. Dasselbe gilt auch für das Ergebnis der wenigen bisher durchgeführten histochemischen Untersuchungen.

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Copyright information

© Springer-Verlag 1965

Authors and Affiliations

  • Erna Christensen
    • 1
    • 2
  • Birthe Palludan
    • 1
    • 2
  1. 1.Department of Physiology, Endocrinology, and Blood-Grouping of the Royal Veterinary and Agricultural CollegeCopenhagenDenmark
  2. 2.University Psychiatric Laboratory (Neuropathology)CopenhagenDenmark

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