Summary
The authors report seven cases of desmoid tumors of the extremities. A tumour less than a few centimetres in size is best removed by wide local excision. Large growths should also be excised, but efforts should be made to preserve the vessels and nerves, since malignant transformation and metastases do not occur. Irradiation therapy should be considered for tumours which are surgically inaccessible. The problems of differential diagnosis between a desmoid tumour and a fibrosarcoma are discussed.
Résumé
Les auteurs rapportent sept cas de tumeurs desmoïdes des extrémités. Une tumeur de volume inférieur à quelques centimètres est traitée au mieux par une large excision locale. Les tumeurs plus volumineuses peuvent également être excisées en s'efforçant de ménager les vaisseaux et les nerfs puisqu'il n'y a pas de risque de transformation maligne ni de metastase. La radiothérapie peut être envisagée lorsque la tumeur est inaccessible à la chirurgie. Discussion des problèmes de diagnostic entre tumeur desmoïde et fibrosarcome.
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References
Brewster RC, Ivins JC (1975) Extra-abdominal desmoid tumours: A clinicopathologic study. J Bone Joint Surg [A] 57: 1026–1031
Couley J, Stout AP, Healy WV (1967) Clinicopathologic analysis of 84 patients with an original diagnosis of fibrosarcoma of the head and neck. Am J Surg 114: 564–569
Dahn I, Jonsson N, Lundh G (1963) Desmoid tumours. A series of 33 cases. Acta Chir Scand 126: 305–314
Dohler JR, Hamelmann H, Lasson U (1984) Aggressive fibromatosen. Chirurg 55: 174–178
Enneking WF (1983) Musculoskeletal tumour surgery. Churchill Livingstone, New York Edinburgh London Melbourne
Enzinger FM, Shiraki M (1967) Musculoaponeurotic fibromatosis of the shoulder girdle (extra-abdominal desmoid). Cancer 20: 1131–1140
Hudson TM, Vandergriend RA, Springfield DS, Hawkins IF, Spanier SS, Enneking WF, Hamlin DJ (1984) Aggressive fibromatosis. Evaluation by CT and angiography. Radiology 150: 494–501
Jauch KW, Löhrs U, Hamperl WD (1983) Die extra-abdominale Fibromatose. Chirurg 54: 690–692
Kinzbrunner B, Ritter S, Domingo J, Rosenthal J (1983) Remission of rapidly growing desmoid tumours after tamoxifen therapy. Cancer 52: 2201–2204
Loch H, Baer U (1980) Desmoid-Tumoren. Med Welt 81: 709–711
MacKenzie DH (1964) Fibroma: a dangerous diagnosis. Review of 205 cases of fibrosarcoma of soft tissues. Brit J Surg 51: 607–612
Meister P, Walcher K, Grabiger A (1973) Desmoid fibroma/aggressive Fibromatosis. Problematik von Behandlung und Verlauf. Münch Med Wochenschr 115: 2025–2031
Pásztor É, Aszódi K (1982) Periosteal desmoid. Magy Traumatol 25: 234–237
Reitano J, Hayry P, Nykyri E, Saxén E (1982) The desmoid tumour. I. Incidence, sex, age — and anatomical distribution in the Finnish population. Am J Clin Pathol 77: 665–673
Rock MG, Pritchard DJ, Reiman HM, Soule EH, Brewster RC (1984) Extra-abdominal desmoid tumours. J Bone Joint Surg [A] 66: 1369–1374
Skaane P, Verhage CCH, Westgard T, Svendsen E (1980) Extra-abdominal desmoid of the axilla. Fortschr Röntgenstr 132: 349–351
Tötterman S, Reiatno JJ (1979) Desmoid tumour: an angiographic study of 5 cases. Br J Radiology 52: 936–941
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Vizkelety, T., Szendröi, M. Desmoid tumours of the extremities. International Orthopaedics 12, 249–253 (1988). https://doi.org/10.1007/BF00547171
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DOI: https://doi.org/10.1007/BF00547171