Neuroradiology

, Volume 25, Issue 4, pp 179–197 | Cite as

The Chiari II malformation: Part IV. The hindbrain deformity

  • T. P. Naidich
  • D. G. McLone
  • K. H. Fulling
Congenital Malformations of the Brain

Summary

Computed tomography successfully delineates the multiple components of the Chiari II malformation at the craniocervical junction, the hindbrain, and the cervical spinal cord. These include wide foramen magnum and upper cervical spinal canal; incomplete fusions of the posterior arches of C1 and lower cervical vertebrae; cascading protrusions of vermis, fourth ventricle, medulla, and cervical cord into the spinal canal; cervicomedullary “kinking”; anterior displacement and sequential sagittal compression of each protrusion by the protrusions posterior to it; compression of all protrusions by the posterior lip of foramen magnum and the posterior arch of C1; and associated cervical hydromyelia, cervical diastematomyelia, and cervical arachnoid cysts.

Key words

Brain, abnormalities cerebellum Chiari II malformation computer tomography, head computed tomography, spine hydrocephalus medulla oblongata myelography, metrizamide myelomeningocele skull, abnormalities spinal cord spine, abnormalities vermis 

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Copyright information

© Springer-Verlag 1983

Authors and Affiliations

  • T. P. Naidich
    • 1
    • 3
  • D. G. McLone
    • 2
    • 3
  • K. H. Fulling
    • 4
  1. 1.Department of RadiologyNorthwestern University Medical SchoolChicagoUSA
  2. 2.Department of Surgery, Division of NeurosurgeryNorthwestern University Medical SchoolChicagoUSA
  3. 3.The Children's Memorial HospitalChicagoUSA
  4. 4.Department of Pathology, Division of NeuropathologyWashington University Medical SchoolSt. LouisUSA

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