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Familiärer Morbus Addison

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Zusammenfassung

Beschreibung von je drei Kindern mit idiopathischem M. Addison in zwei Familien, die als Kusins zweiten Grades miteinander verwandt sind. Literaturübersicht der bekannten familiären Fälle von primär chronischidiopathischer Nebennierenrindeninsuffizienz. Genetische Analyse des uns bekannten Materials. In der Mehrzahl der Fälle scheint der Erbgang autosomal-recessiv zu sein.

Summary

Description of six children in two families (three in each) with idiopathic Addisons disease, related as second cousins. Information about published familial cases of chronic idiopathic insufficiency of adrenal glands. In most of the cases heredity seems to be of the autosomalerecessive type.

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  1. Kinderklinik des Kantonsspitals Aarau, (Schweiz)

    Fritz Nöthiger

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Nöthiger, F. Familiärer Morbus Addison. Z. Kinder-Heilk. 99, 14–32 (1967). https://doi.org/10.1007/BF00517818

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