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Partial abnormal pulmonary venous return in Turner syndrome

  • Cardiology
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Abstract

Three cases of partial anomalous pulmonary venous return, in one case combined with coarctation of the aorta and in another with discrete subaortic stenosis, are described in patients with Turner syndrome. In two of them the right and left superior pulmonary veins drained into the right superior vena cava and left innominate vein respectively. Remarkably, in all three cases the atrial septum was intact. We feel that this unique combination probably is not purely coincidental, but might rather be specific for Turner syndrome.

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Abbreviations

AI:

aortic insufficiency

ASD:

atrial septal defect

PAPVR:

partial abnormal pulmonary venous return

SVC:

superior vena cava

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van Wassenaer, A.G., Lubbers, L.J. & Losekoot, G. Partial abnormal pulmonary venous return in Turner syndrome. Eur J Pediatr 148, 101–103 (1988). https://doi.org/10.1007/BF00445912

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  • DOI: https://doi.org/10.1007/BF00445912

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