Abstract
Three cases of partial anomalous pulmonary venous return, in one case combined with coarctation of the aorta and in another with discrete subaortic stenosis, are described in patients with Turner syndrome. In two of them the right and left superior pulmonary veins drained into the right superior vena cava and left innominate vein respectively. Remarkably, in all three cases the atrial septum was intact. We feel that this unique combination probably is not purely coincidental, but might rather be specific for Turner syndrome.
Similar content being viewed by others
Abbreviations
- AI:
-
aortic insufficiency
- ASD:
-
atrial septal defect
- PAPVR:
-
partial abnormal pulmonary venous return
- SVC:
-
superior vena cava
References
Goldberg MB, Sculley AL, Soloman IL, Steinbach HLMD (1968) Gonadal dysgenesis in phenotypic female subject. Am J Med 45: 529–543
Hughes CW, Rummer PC (1944) Anomalous pulmonary veins. Arch Pathol 37:364–366
Lebeque P, Bosi G, Lintermans J, Stijns M, Germanes J, Chalant CH, Vliers A (1984) Myxomatous degeneration of the mitral valve in a child with Turner syndrome and partial anomalous pulmonary venous return. Eur J Pediatr 141:228–230
Nora JJ (1983) Etiologic aspects of heart diseases. In: Adams FH, Emmaniouillides GC (eds) Moss' heart disease in infants, children and adolescents, 3rd edn. Williams and Wilkins, Baltimore, pp 2–10
Price WH, Willey RF (1980) Partial anomalous pulmonary venous drainage in two patients with Turner's syndrome. J Med Gen 17: 133–134
Snellen HA, Ingen van HC, Hoefsmit ECM (1968) Patterns of anomalous pulmonary venous drainage. Circulation 38:45–63
Tourniaire MMJ, Tourniaire A, Tartulier M, Robert M (1969) Syndrome de Turner avec retour veineux pulmonaire anormal partiel et communication interauriculair. Rev Lyon Med 18:95–100
Uhrenholdt A, Wilton Djernes B, Efsen E (1975) Partial anomalous venous drainage in a patient with Turner's syndrome. Dan Med Bull 22:37–39
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
van Wassenaer, A.G., Lubbers, L.J. & Losekoot, G. Partial abnormal pulmonary venous return in Turner syndrome. Eur J Pediatr 148, 101–103 (1988). https://doi.org/10.1007/BF00445912
Received:
Accepted:
Issue Date:
DOI: https://doi.org/10.1007/BF00445912