Abstract
A case of chronic lymphadenopathy and splenomegaly existing over a period of 11 years, with a variety of acquired deficiencies of immunity and autoimmune phenomena, is described. It is almost identical with the 5 children reported in 1967 by Canale and Smith as a new benign syndrome “chronic lymphadenopathy simulating malignant lymphoma”. The relationship to similar disorders with lymphadenopathy and immunological abnormalities is discussed.
Zusammenfassung
Von Canale u. Smith wurde 1967 an Hand von 5 kindlichen Fällen eine benigne lymphoproliferative Erkrankung — einhergehend mit chronischer Lymphadenopathie, Splenomegalie, variablen erworbenen Immunveränderungen und Autoimmunphänomenen — beschrieben. Befunde und 11 jährige Verlaufsbeobachtung eines ähnlichen Falles werden dargestellt und die Beziehungen zu verwandten, pseudomalignen und malignen Lymphadenopathien diskutiert.
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Kellerer, K., Mutz, I. Chronische pseudomaligne immunproliferation (Canale-Smith-Syndrom). Eur J Pediatr 121, 203–213 (1976). https://doi.org/10.1007/BF00445483
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DOI: https://doi.org/10.1007/BF00445483