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European Journal of Pediatrics

, Volume 136, Issue 3, pp 311–316 | Cite as

Dysplasia epiphysealis hemimelica—Trevor disease. Severe manifestations in a child

  • H. -R. Wiedemann
  • M. Mann
  • P. Spreter v. Kreudenstein
Case Reports

Abstract

This report describes a case of “dysplasia epiphysealis hemimelica” with the first clinical manifestations at birth and increasing difference in the length of the lower extremities during infancy. The diagnosis was made at the age of 3 years when marked disability had already occurred. There was involvement of both legs and, to a lesser degree, the arms suggesting that this is a systemic disorder.

Key words

Bones, growth and development Bones, osteochondrodysplasias Epiphyses Skeletal system, dysplasia epiphysealis hemimelica Trevor disease 

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Copyright information

© Springer-Verlag 1981

Authors and Affiliations

  • H. -R. Wiedemann
    • 1
  • M. Mann
    • 2
  • P. Spreter v. Kreudenstein
    • 1
  1. 1.Department of PediatricsUniversity of KielKielFRG
  2. 2.Department of OrthopaedicsUniversity of KielGermany

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