Abstract
Secondary cystathioninuria was found in two of 46 children suffering from tumors, leukemia, liver diseases, inherited metabolic disorders, cystic fibrosis and celiac disease. Of these two patients, one had congenital biliary atresia and the other cytomegalovirus infection. Seven further children had only moderately elevated excretion of cystathionine. It is suggested that secondary cystathioninuria is uncommon in the diseases investigated.
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Endres, W., Schaub, J., Bremer, H. J., Grütte, E: Sekundäre Cystathioninurie. Z. Kinderheilk. 110, 46–58 (1971)
Endres, W., Seibold, H.: Renal excretion of cystathionine and creatinine in humans at different ages. Clin. Chim. Acta (in press)
Fourman, P., Summerscales, J. W., Morgan, D. M.: Cystathioninuria from pyridoxine deficiency complicating treatment of hypercalcaemia in a cretin. Arch. Dis. Childh. 41, 273–278 (1966)
Geiser, C. F., Efron, M. L.: Cystathioninuria in patients with neuroblastoma or ganglioneuroblastoma. Its correlation to vanilmandelic acid excretion and its value in diagnosis and therapy. Cancer 22, 856–860 (1968)
Gjessing, L. R.: Cystathioninuria and vanil-lactic-acid-uria in neuroblastoma and argentaffinoma. Lancet 1963 II, 1281–1282
Gjessing, L. R., Mauritzen, K.: Cystathioninuria in hepatoblastoma. Scand. J. Clin. Lab. Invest. 17, 513–514 (1965)
Gjessing, L. R.: Cystathioninuria and vanil-lactic-acid-uria. Recent results in cancer research 2, 26–33. Berlin-Heidelberg-New York: Springer 1966
Lieberman, E., Shaw, K. N. F., Donnell, G. N.: Cystathioninuria in galactosemia and certain types of liver disease. Pediatrics 40, 828–833 (1967)
Scriver, C. R., Hutchison, J. H.: The vitamin B6 deficiency syndrome in human infancy: Biochemical and clinical observations. Pediatrics 31, 240–250 (1963)
Shaw, K. N. F., Lieberman, E., Koch, R., Donnell, G. N.: Cystathioninuria. Amer. J. Dis. Child. 113, 119–128 (1967)
Studnitz, W. v: Secondary cystathioninuria. Acta Paediat. Scand. 58, 173–177 (1969)
Studnitz, W. v.: Cystathioninuria in children with neuroblastoma with and without metastasis. Acta Paediat. Scand. 59, 80–82 (1970)
Voute, P. A., Jr., Wadman, S. K.: Cystathioninuria in hepatoblastoma. Clin. Chim. Acta 22, 373–378 (1968)
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Dedicated to Professor Dr. A. Wiskott on the occasion of his 80th birthday
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Endres, W., Wuttge, B. Occurrence of secondary cystathioninuria in children with inherited metabolic disorders, liver diseases, neoplasms, cystic fibrosis and celiac disease. Eur J Pediatr 129, 29–35 (1978). https://doi.org/10.1007/BF00441371
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DOI: https://doi.org/10.1007/BF00441371