Virchows Archiv A

, Volume 388, Issue 1, pp 39–49 | Cite as

Double inlet right ventricle

Report of a case and review of the literature
  • J. N. Cox
  • P. Bopp
  • E. Hauf
Original Articles


A case of double inlet right ventricle in which both atrioventricular valves opened completely into the right ventricle is described. The left atrium communicated with the right ventricle by way of an opening low in the atrial septum and there was a large ventricular septal defect. The pulmonary trunk and aorta took their origin from the right and hypoplastic left ventricles respectively. The literature on this rare cardiac anomaly is reviewed and the morphological findings in this case are compared with those of the recorded cases. A short discussion of the possible embryogenesis is given.

Key words

Double inlet right ventricle Straddling mitral valve Double outlet right ventricle Common ventricle 


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Copyright information

© Springer-Verlag 1980

Authors and Affiliations

  • J. N. Cox
    • 1
  • P. Bopp
    • 1
  • E. Hauf
    • 1
  1. 1.Departments of Pathology and Medicine (Division of Cardiology) and Cardiovascular SurgeryGenevaSwitzerland

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