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Congenital aggressive lipomatosis

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Abstract

Three cases of congenital lipomatosis involving the thoracic region posteriorly are presented delineating the natural history of the disease and depicting underlying bone and soft tissue changes. The rib widening and pleural thickening appear to be related to increased intercostal vascularity feeding the overlying tumor, as delineated by angiography. This entity is not described in the radiologic literature.

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Lachman, R.S., Finklestein, J., Mehringer, C.M. et al. Congenital aggressive lipomatosis. Skeletal Radiol 9, 248–254 (1983). https://doi.org/10.1007/BF00354126

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  • DOI: https://doi.org/10.1007/BF00354126

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