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Computerized tomography in primary hyperammonemia

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Summary

Urea cycle enzymophathies are rare in the literature. They are accompanied by neurological disorders somehow related to the increase in blood ammonia. Reviewing the possible physiopathological course we present a case in which during an eight month period severe cerebral atrophy developed, more intense in the occipital region but totally sparing the posterior cranial fossa structures.

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Authors and Affiliations

  1. Department of Neuroradiology, Hospital de Navarra, Pamplona, Navarra, Spain

    J. Olier

  2. Department of Neurology, Hospital de Navarra, Pamploma, Navarra, Spain

    J. Gallego & E. Digon

Authors
  1. J. Olier
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  2. J. Gallego
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  3. E. Digon
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Olier, J., Gallego, J. & Digon, E. Computerized tomography in primary hyperammonemia. Neuroradiology 31, 356–357 (1989). https://doi.org/10.1007/BF00344184

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  • DOI: https://doi.org/10.1007/BF00344184

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