Summary
A 60-year-old woman affected by myasthenia gravis with onset at 27 years is described. At the age of 54 years the patient showed amyotrophy of the shoulders and of the legs with bilateral “steppage”. There was a gradual worsening and progression of the atrophy to other muscles. The nature of the disease is discussed following EMG and histologic data.
Zusammenfassung
Es wird eine 60jährige Frau, die an Myasthenia gravis leidet, beschrieben. Die Krankheit begann, als sie 27 Jahre alt war. Mit 54 Jahren zeigte die Patientin eine Myatrophie der Schulter und der Beine mit bilateralem Steppengang. Zunehmende Verschlechterung und Übergreifen der Atrophie auf andere Muskelgebiete. Die Natur der Krankheit wird auf der Basis der EMG und der histologischen Befunde besprochen.
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Negri, S., Caraceni, T. & Cornelio, F. A case of myasthenia gravis with neurogenic amyotrophy. Z. Neurol. 205, 115–122 (1973). https://doi.org/10.1007/BF00316015
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DOI: https://doi.org/10.1007/BF00316015