Summary
The clinicopathological findings in a child with extraskeletal Ewing sarcoma are described.
The patient complained of pain in the lower back and difficulty walking. An extraskeletal, epidural, friable tumor, 2–3 cm long was removed from the epidural space. It had no relationship with the bone structures. Light and electron microscopic examination of the tumor led to the diagnosis of Ewing sarcoma. The morphological aspects of this neoplasia and the problem of the differential diagnosis with other small cell tumors of the epidural space are discussed.
Zusammenfassung
Es wird ein Ewing-Sarcom, welches sich außerhalb des Skelettes bei einem Kind entwickelte, geschildert. Klinisch manifestierte es sich als epidurale Masse. Bei der chirurgischen Exploration zeigte sich ein brüchiges Gewebe, welches 2–3 cm lang war und nicht vom Knochen ausging. Lichtmikroskopisch und elektronenmikroskopisch ließ sich die Diagnose eines Ewing-Sarcoms stellen.
Es werden morphologische Aspekte und differentialdiagnostische Überlegungen in Zusammenhang mit Tumoren des Epiduralraumes diskutiert.
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Simonati, A., Vio, M., Iannucci, A.M. et al. Lumbar epidural ewing sarcoma. J Neurol 225, 67–72 (1981). https://doi.org/10.1007/BF00313464
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DOI: https://doi.org/10.1007/BF00313464