Abstract
A 40-year-old woman with Peutz-Jeghers syndrome and an appendiceal intussusception is reported. In this patient, the lead point was a large sessile, appendiceal polyp. The invaginated and inverted portion of the appendix resembled the long stalk of a pedunculated polyp on roentgenography and endoscopic examination. Histologically, the appendiceal polyp was a villous adenoma with mild to severe atypia and focal carcinoma in situ. In patients with Peutz-Jeghers syndrome, hamartomatous polyps and colorectal adenomatous polyps with highly malignant potential can coexist and must be managed appropriately. Therefore, when evaluating a polypoid or a pedunculated lesion in the cecal lumen, the possibility of an appendiceal intussusception should also be investigated.
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Miyahara, M., Saito, T., Etoh, K. et al. Appendiceal intussusception due to an appendiceal malignant polyp — An association in a patient with peutz-jeghers syndrome: Report of a case. Surg Today 25, 834–837 (1995). https://doi.org/10.1007/BF00311463
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DOI: https://doi.org/10.1007/BF00311463