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Giant pigmented hairy nevus in two siblings

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Summary

The case of a 14-month-old girl with a giant pigmented hairy nevus of the “bathing trunk” type and multiple satellite lesions is presented. We also report on her 2 1/2 year-old brother with a solitary large pigmented hairy nevus on his right wrist. The significance of this type of nevus in relation to neurocutaneous melanosis is stressed, and the possible role of hereditary factors in this rare syndrome is discussed.

Zusammenfassung

Es wird über den Fall eines 14 Monate alten Mädchens mit einem hosenförmigen Tierfellnaevus und zahlreichen Satellitennaevi berichtet, dessen 2 1/2jähriger Bruder einen ausgedehnten behaarten Pigmentnaevus über dem rechten Handgelenk zeigt. Die Bedeutung dieses besonderen Naevustyps im Rahmen der neurocutanen Melanose wird hervorgehoben und genetische Aspekte bei diesem seltenen Syndrom erörtert.

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Authors and Affiliations

  1. Universitäts-Hautklinik, Heidelberg

    V. Voigtländer & E. G. Jung

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  1. V. Voigtländer
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  2. E. G. Jung
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With support of the Deutsche Forschungsgemeinschaft, Sonderforschungsbereich Nr. 35 “Klinische Genetik”.

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Voigtländer, V., Jung, E.G. Giant pigmented hairy nevus in two siblings. Hum Genet 24, 79–84 (1974). https://doi.org/10.1007/BF00281112

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