Abstract
Systemic-to-pulmonary collateral vessels and shunts develop in patients with isolated unilateral absence of a pulmonary artery (IUAPA). Two cases of IUAPA (right and left) with hemoptysis in adult life are presented. Selective embolization of these systemic vessels controlled hemoptysis successfully. These cases represent an example of an alternative treatment for this rare anomaly.
Similar content being viewed by others
References
Bahler RC, Carson P, Traks E, Levene A, Gillespie D (1969) Absent right pulmonary artery. Problems in diagnosis and management. Am J Med 46:64–71
Ko T, Gatz MG, Reisz GR (1990) Congenital unilateral absence of a pulmonary artery: A report of two adult cases. Am Rev Respir Dis 141:795–798
Arriero JM, Gil J, Martin C, Mainar V, Romero S (1991) Unilateral absence of a pulmonary artery: Congenital disease or embolie occlusion? Eur Respir J 4:1299–1300
Mehta AC, Livingston DR, Kawalek W, Golish JA, O'Donnell JK (1987) Pulmonary artery agenesis presenting as massive hemoptysis. A case report. Angiology 38:67–71
Gluck MC, Moser KM (1970) Pulmonary artery agenesis. Diagnosis with ventilation and perfusion scintiphotography. Circulation 41:859–867
Schamroth CL, Sareli P, Dean H (1987) Combined unilateral pulmonary artery agenesis and contralateral peripheral pulmonary artery stenosis. Clin Cardiol 10:363–366
Canver CC, Pigott JD, Mentzer RM (1991) Neonatal pneumonectomy for isolated unilateral pulmonary artery agenesis. Ann Thorac Surg 52:294–295
Morales P, Miravet L, Marco V (1991) Agenesis of the right pulmonary artery in a young asymptomatic girl. Eur Respir J 4:1301–1302
Cogswell TL, Singh S (1986) Agenesis of the left pulmonary artery as a cause of hemoptysis. Angiology 37:154–159
Stiller RJ, Soberman S, Turetsky A, Lockwood C, Haddad R (1988) Agenesis of the pulmonary artery: An unusual cause of dyspnea in pregnancy. Am J Obstet Gynecol 158:172–173
Pool PE, Vogel JK, Blount SG (1962) Congenital unilateral absence of a pulmonary artery. The importance of flow in pulmonary hypertension. Am J Cardiol 10:706–732
Hübsch P, Pichler W, Lang I, Miczoch J (1987) Isolierte Agenesie der rechten Pulmonalarterie mit später Manifestation einer pulmonalarteriellen Hypertension. Röntgen-Bl 40:23–25
Kleinman PK (1979) Pleural telangiectasia and absence of a pulmonary artery. Radiology 132:281–284
Uflacker R, Kaemmerer A, Picon PD, Rizzon CF, Neves C, Oliveira E, Oliveira ME, Azevedo S, Ossanai R (1985) Bronchial artery embolization in the management of hemoptysis: Technical aspects and long-term results. Radiology 157:637–644
Lois JF, Gomes AS, Smith DC, Laks H (1988) Systemic-to-pulmonary collateral vessels and shunts: Treatment with embolization. Radiology 169:671–676
Moser KM, Olson LK, Schlusselberg M, Daily PO, Deembitsky WP (1989) Chronic thromboembolic occlusion in the adult can mimic pulmonary artery agenesis. Chest 95:503–508
Toews WH, Pappas G (1983) Surgical management of absent right pulmonary artery with associated pulmonary hypertension. Chest 84(4):497–499
Hemingway AP, Allison DJ (1988) Complications of embolization: Analysis of 410 procedures. Radiology 166:669–672
Author information
Authors and Affiliations
Rights and permissions
About this article
Cite this article
Reñé, M., Sans, J., Dominguez, J. et al. Unilateral pulmonary artery agenesis presenting with hemoptysis: Treatment by embolization of systemic collaterals. Cardiovasc Intervent Radiol 18, 251–254 (1995). https://doi.org/10.1007/BF00239422
Issue Date:
DOI: https://doi.org/10.1007/BF00239422