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Progressive hemifacial atrophy: historical review and actual features related to a new classification of facial hypoplasia and atrophy

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Summary

Progressive hemifacial atrophy, described initially by Parry and Romberg, is reviewed in terms of etiopathogenesis and clinical features. The purpose is to clarify the variegated nature of this syndrome and to distinguish it from other forms of atrophy affecting the face, principally the soft tissues. The authors propose a new general classification of hypoplasia and atrophy of the face.

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Authors and Affiliations

  1. Department of Plastic and Reconstructive Surgery, University Hospital Rotterdam, Dijkzigt and Sophia Children's Hospital, Rotterdam, The Netherlands

    R. Roddi, P. M. Gilbert & J. C. H. van der Meulen

  2. Department of Plastic and Reconstructive Surgery, University Hospital Milan, S. Donato Hospital, Milan, Italy

    E. Riggio

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  1. R. Roddi
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  2. E. Riggio
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  4. J. C. H. van der Meulen
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Roddi, R., Riggio, E., Gilbert, P.M. et al. Progressive hemifacial atrophy: historical review and actual features related to a new classification of facial hypoplasia and atrophy. Eur J Plast Surg 17, 178–183 (1994). https://doi.org/10.1007/BF00188556

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