Summary
Romberg's disease, or hemifacial atrophy, is a well known but rare disorder of unknown etiology. The literature is replete with descriptions of the soft tissue deformity and its correction; however, there is little information about the bony abnormalities with comparison to the soft tissue deficit. Five patients with moderate to severe progressive hemifacial atrophy were evaluated by 3 dimensional CT scan reformatting. Atrophy of bone and soft tissue was noted in all patients in the study.
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Smith, R.J., Jackson, I.T., Xiao, H. et al. 3-D CT scan measured bony deficiency of the facial skeleton in progressive hemifacial atrophy. Eur J Plast Surg 17, 292–297 (1994). https://doi.org/10.1007/BF00181094
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DOI: https://doi.org/10.1007/BF00181094