Abstract
A follow-up study has been performed on children treated for Hirschsprung's disease who also had mental retardation. There were nine children with Down's syndrome and one with minimal brain damage. The ten children were reviewed with special consideration to their bowel habits. Strikingly poor results were found: two of the ten children had gained voluntary bowel control, one during the first 6 months postoperatively, the other after 9 years of soiling and recurrent episodes of enterocolitis. The remaining eight children had soiling although two were improving after 12 and 14 years respectively.
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Molander, ML. Hirschsprung's disease in mentally retarded patients: a bad prognostic combination. Pediatr Surg Int 5, 339–340 (1990). https://doi.org/10.1007/BF00177101
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DOI: https://doi.org/10.1007/BF00177101