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Poland syndrome with exomphalos major

A successful management strategy

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Abstract

Assessment of the effects of closure of exomphalos on ventilatory mechanics is pivotal to primary management decisions. We present a patient in whom problems of abdominovisceral disproportion were compounded by reduced thoracic volume due to Poland's syndrome. Initial non-operative management with delayed closure of the ventral hernia using epidural anaesthesia was successful.

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Authors and Affiliations

  1. Department of Paediatric Surgery, University of Natal, Congella 4013, P.O. Box 17039, Durban, Natal, South Africa

    G. P. Hadley

  2. Department of Anaesthetics, University of Natal, Congella 4013, P.O. Box 17039, Durban, Natal, South Africa

    A. T. Bösenberg

Authors
  1. G. P. Hadley
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  2. A. T. Bösenberg
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Hadley, G.P., Bösenberg, A.T. Poland syndrome with exomphalos major. Pediatr Surg Int 10, 498–500 (1995). https://doi.org/10.1007/BF00176398

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  • DOI: https://doi.org/10.1007/BF00176398

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