Abstract
Several congenital anomalies of the portal vein and inferior vena cava (IVC) have been reported; however, reports of a congenital communication between the portal vein and IVC are few. We report a patient who was found to have a natural shunt between the extrahepatic portal vein and the IVC that was discovered when she underwent a right hepatic lobectomy for an undifferentiated liver sarcoma. The patient also had agenesis of the right kidney. We have not been able to find a similar case reported in English literature.
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Shah, R., Ford, E.G. & Woolley, M.M. Congenital portocaval shunt. Pediatr Surg Int 7, 216–217 (1992). https://doi.org/10.1007/BF00175845
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DOI: https://doi.org/10.1007/BF00175845